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Updated: Jul 16, 2025

Rapid One-step Enzymatic Synthesis and All-aqueous Purification of Trehalose Analogues
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在患有多重硫酶缺乏症的患者中,静脉注射三糖的效果

Shabnam Radbakhsh1, Moein Mobini2, Eric Gumpricht3

  • 1Student Research Committee, Mashhad University of Medical Sciences, Mashhad, Iran.

Archives of medical science : AMS
|September 21, 2023
PubMed
概括

对患有多重硫酶缺乏症 (MSD) 的儿童进行静脉注射三糖治疗,显示生活质量和脏大小有所改善. 需要进一步的研究来证实三糖在MSD患者的疗效.

关键词:
lysosomal 储存疾病 lysosomal 储存疾病多重硫酸盐酶缺乏症多重硫酸酶缺乏症这是一种三糖.

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