在儿科心律失常性心肌病的ICD结局
Marianna Cicenia1, Massimo Stefano Silvetti1, Nicoletta Cantarutti1
1Pediatric Cardiology and Arrhythmia/Syncope Complex Unit, Bambino Gesù Children's Hospital, IRCCS, Rome, Italy.
International journal of cardiology
|September 22, 2023
概括
植入式心脏转换器-除器 (ICD) 对儿科心律失常性心肌病 (ACM) 患者是安全有效的. 虽然在初级预防中很少有适当的疗法,但在二级预防中它们很常见,并发症很少.
科学领域:
- 心脏病学 心脏病学
- 儿科电子生理学 儿科电子生理学
- 遗传性心脏疾病 遗传性心脏疾病
背景情况:
- 节律失调性心肌病变 (ACM) 是一种罕见的儿科疾病.
- 突然心脏死亡 (SCD) 是主要的风险,通常需要植入可植入心脏转换器-除器 (ICD) 植入.
- 在儿科ACM中评估ICD结果至关重要.
研究的目的:
- 评估ICD植入在儿科ACM患者中的安全性和有效性.
- 分析这一群体中的并发症率和干预结果.
- 为儿童ACM中的ICD治疗指南提供证据.
主要方法:
- 对自2009年以来接受ICD的儿科ACM患者 (18岁以下) 的回顾性分析.
- 根据当前的建议和指导方针进行包容.
- 随访期间记录的结果,包括适当/不适当的冲击和并发症.
主要成果:
- 19名儿科ACM患者接受了ICD;79%是皮下ICD (S-ICD).
- 对21%的患者 (13%的初级预防,50%的二级预防) 进行了适合心室低心率 (VT) 的ICD干预.
- 不适当的冲击 (10.5%) 和设备并发症 (16%) 是罕见的,大多与伤口有关.
结论:
- 在儿科ACM患者中,ICD治疗是有效和安全的.
- 在初级预防中,适当的疗法不太常见,但在二级预防中却很常见.
- 不适当的冲击和设备并发症的低率支持在这个人群中使用ICD.
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