扩散性桑托格兰瘤性皮叶龙炎:一种罕见的疾病,具有常见的表现.
Ahmed Gamal Sayed1, Tafe Badghaish1, Nivan Abdo2
1College of Medicine, Alfaisal University, Riyadh, SAU.
Cureus
|September 26, 2023
概括
桑托格兰瘤性炎 (XGP) 是一种罕见的病,导致炎症和破坏. 早期CT诊断和切除术是治疗尿路症状的儿童的关键.
科学领域:
- 腎臟病學 (nephrology) 是一種醫學專業.
- 儿科泌尿外科 儿科泌尿外科
- 病理学 病理学 病理学
背景情况:
- 桑托格兰瘤性炎 (XGP) 是一种罕见的,具有破坏性的炎性疾病.
- 它的特点是慢性颗粒状变化,通常与尿路异常有关,如阻塞或感染.
- XGP可能会被误认为是脏瘤,因此需要准确的差异诊断.
研究的目的:
- 提交一个儿童被诊断为Xanthogranulomatous pyelonephritis的病例报告.
- 突出XGP的临床表现,诊断成像和组织病理学发现.
- 强调在儿童腹部质量和尿路感染的差异诊断中考虑XGP的重要性.
主要方法:
- 一个儿科患者的病例介绍,症状包括发烧,腹痛,吐,厌食症和体重减轻.
- 腹部计算机断层扫描 (CT) 显示了多部位的囊性病变与化和psoas肌肉.
- 脏的组织病理学检查证实了XGP的特征,包括含脂质的巨细胞和多核巨细胞.
主要成果:
- 这种psoas肌肉的检测结果为大肠杆菌阳性.
- 组织病理学证实了Xanthogranulomatous pyelonephritis的发生.
- 患者接受了切除术和腹疏通.
结论:
- 桑托格拉诺瘤性肌炎是一种罕见的实体,需要在患有发烧和尿路症状的儿童中加以考虑.
- 计算机断层扫描 (CT) 对于早期诊断至关重要.
- 切除术是XGP的最终治疗方法.
相关概念视频
01:27Acute Pyelonephritis I: Introduction
20
Pyelonephritis is a bacterial infection that primarily affects the renal parenchyma and collecting system, including the renal pelvis, tubules, and interstitial tissue of one or both kidneys. It can be classified as either acute—a sudden, severe infection—or chronic, which refers to long-term or recurrent kidney infections.The primary cause of acute pyelonephritis (APN) is bacterial infection, with Escherichia coli accounting for approximately 70-80% of cases. Other bacteria, such...
20
01:28Acute Pyelonephritis II: Diagnostic Studies and Management
15
Introduction:For diagnosing acute pyelonephritis, a comprehensive patient history is collected to identify symptoms such as dysuria, frequent or urgent urination, flank pain, or costovertebral angle (CVA) tenderness that may suggest a kidney infection.Physical ExaminationDuring the physical examination, CVA tenderness is assessed. This involves gentle percussion over the costovertebral angle, where tenderness often indicates a kidney infection.Diagnostic TestsUrinalysis: Used to identify white...
15
01:24Nephrotic Syndrome I : Introduction
9
Nephrotic Syndrome is a chronic kidney disorder defined by clinical findings such as severe proteinuria, hypoalbuminemia, hyperlipidemia, and edema. These symptoms result from damage to the glomeruli, the kidney’s filtering units, increasing their permeability to proteins.Definition and Meaning:Proteinuria, defined as the loss of more than 3.5 grams of protein per day in adults, is a crucial feature of nephrotic syndrome. This condition is often accompanied by edema, the accumulation of...
9
01:31Pulmonary Tuberculosis III
357
Tuberculosis (TB) is a contagious infection primarily affecting the lung parenchyma but which can also affect other body parts. TB can be classified based on disease development, presentation, and the affected anatomical site.
The first classification is based on the development of the disease, and it includes the following categories:
The first classification is based on the development of the disease, and it includes the following categories:
357
01:25Urinary Tract Infection II: Pathophysiology
18
The pathophysiology of urinary tract infections (UTIs) encompasses several progressive stages, beginning with bacterial colonization and culminating in potential systemic complications if untreated. UTIs are primarily initiated by bacteria, such as Escherichia coli, which often originate from the gastrointestinal tract and migrate to the urinary system through the periurethral area. This migration can occur via several routes, including improper hygiene practices, sexual activity, or...
18
01:10Nephrons
2.7K
The kidneys are intricate organs with millions of working units known as nephrons. Each nephron features two major structures: the renal corpuscle, which facilitates blood plasma filtration, and the renal tubule, which handles the glomerular filtrate. Blood supply is directly linked to the nephrons. The renal corpuscle consists of the glomerulus, a capillary network, and the Bowman's capsule, a double-walled epithelial structure that encases the glomerulus. The filtering of blood plasma...
2.7K