无症状的基本血栓细胞瘤与肝外门静脉血栓形成:一个病例报告
Yoshikazu Yakami1, Toshihiko Yagyu2, Tomoki Bando2
1Department of Internal Medicine, Komatsu Hospital, Neyagawa, Osaka, Japan.
The American journal of case reports
|September 28, 2023
概括
本质性血栓细胞瘤 (ET),一种骨髓增殖性瘤,可以导致额外门静脉血栓瘤 (EHPVT). 这个案例突出了一个无症状的患者,JAK2阳性ET和EHPVT,强调需要考虑ET在EHPVT诊断中.
科学领域:
- 血液学 血液学 血液学
- 在瘤学瘤学.
- 内部医学 内部医学
背景情况:
- 基本血栓细胞瘤 (ET) 是一种由血小板的过度产生而表现出的骨髓增殖性瘤.
- 简氏激酶2 (JAK2) 突变存在于约60%的ET病例中,并与血栓形成的风险增加有关.
- ET可以导致系统性血栓事件,包括外门静脉血栓症 (EHPVT).
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