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Updated: Jul 14, 2025

Adoptive Immunotherapy of iNKT Cells in Glucose-6-Phosphate Isomerase G6PI-Induced RA Mice
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在三名患有SAVI综合征的患者中,在Janus激酶抑制剂下进行肺移植

Kenza Rhzioual Berrada1, Alexandre Belot2,3,4, Bénédicte Neven5

  • 1Service de Pneumologie Pédiatrique, Hôpital Femme-Mère-Enfant, Hospices Civils de Lyon, Lyon, France.

Journal of clinical immunology
|October 9, 2023
PubMed
概括

兴奋剂干扰素基因 (STING) 与婴儿发病相关的血管病变 (SAVI) 是一种罕见的自身炎症性疾病. 在肺移植 (LT) 之前,ruxolitinib可能会改善SAVI患者的呼吸状况.

关键词:
自动炎症性疾病 自动炎症性疾病雅克抑制剂的使用这就是SAVI综合征.TMEM173/STING1 的意思是什么?肺移植是什么意思?

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