相关实验视频
Updated: Jul 13, 2025

08:09
Vessel-sparing Excision and Primary Anastomosis
Published on: January 7, 2019
11.5K
长期管理的问题在Cloacal外:一个单一机构审查
Nora M Haney1, Christian C Morrill1, Ahmad Haffar1
1James Buchanan Brady Urological Institute, Division of Pediatric Urology, Douglas A. Canning MD Exstrophy Database Center, Charlotte Bloomberg Children's Hospital, The Johns Hopkins Medical Institutions, Baltimore, MD, USA.
Journal of pediatric surgery
|October 14, 2023
概括
克洛亚克外缩症 (CE) 患者经历了显著的长期健康问题,但可以实现独立的生活. 护理方面的进步改善了结果,尽管面临挑战,但许多成年人仍在工作和接受教育.
科学领域:
- 儿科手术 儿科手术
- 泌尿器科 泌尿器科 泌尿器科 泌尿器科
- 胃肠病学 胃肠病学
- 整形外科 整形外科 整形外科
- 心理学 心理学 心理学
背景情况:
- 克洛亚克外 (CE) 是外-表皮综合体内最严重的先天性形.
- 这项研究调查了大量患者队列中的长期后果.
研究的目的:
- 分析10岁以上的外 (CE) 患者的生殖尿道,胃肠道,骨科和心理社会结果.
- 为了评估CE幸存者的长期功能状态和生活质量.
主要方法:
- 从1974年到2023年,对145名克洛亚克外 (CE) 患者的前性维护数据库进行了审查 (在1490名外表皮病频谱患者中).
- 分析的重点是CE患者,随访时间至少为10年,评估各种功能结果.
主要成果:
- 在≥10年随访的63名CE患者中,许多人有大肠导管 (71.4%) 和成功的肠道管理 (58.7%的结肠术,PSARP后60%的大肠).
- 显著的轮椅使用 (34.9%) 和心理社会诊断 (52.4%焦虑/抑郁,27.0%慢性疼痛) 被注意到,但75%的ADL是独立的.
- 成年CE患者的大学入学率高 (79.5%) 和就业率高 (82.1%).
结论:
- 尽管在多个器官系统中出现了长期的后果,但护理方面的进步使CE患者的存活率接近100%.
- 许多患有外的个体有独立和功能性的成年生活,这突显了综合管理策略的有效性.
相关概念视频
Inflammatory Bowel Disease V: Surgical Management
161
Surgical interventions for inflammatory bowel disease (IBD), which includes ulcerative colitis and Crohn's disease, are essential in managing symptoms and addressing complications. The selection of surgical procedures is contingent upon the specific conditions and complications that stem from these illnesses.
Here are some common surgical interventions for IBD:
Here are some common surgical interventions for IBD:
161
Urinary Tract Calculi VI: Surgical Management
8
Procedures for Kidney StonesMedical intervention is necessary when kidney stones or renal calculi are too large to pass spontaneously (typically greater than 5 millimeters) when stones are accompanied by symptomatic infection (such as fever or pyelonephritis), when they impair kidney function, or when they cause persistent symptoms like severe pain, nausea, or urinary retention. Additionally, patients with only one kidney or those who cannot be treated with medical management also require...
8
Ostomy Care
330
Introduction
An ostomy is a surgical procedure that creates an artificial opening from the intestines to the outside of the body, allowing for the rerouting of effluent. This opening is known as a stoma. A stoma usually protrudes above the skin surface, appearing pink or red, moist, and round, and it lacks nerve sensations.
There are different types of ostomies, including colostomies, ileostomies, and urostomies:
An ostomy is a surgical procedure that creates an artificial opening from the intestines to the outside of the body, allowing for the rerouting of effluent. This opening is known as a stoma. A stoma usually protrudes above the skin surface, appearing pink or red, moist, and round, and it lacks nerve sensations.
There are different types of ostomies, including colostomies, ileostomies, and urostomies:
330
Appendicitis-II: Diagnostic Studies and Management
81
Diagnosing and managing appendicitis requires a structured and comprehensive approach that spans from initial assessment to postoperative care. Here is an overview of the process:
Diagnosing Appendicitis
It requires a multifaceted approach, starting with a detailed physical examination to pinpoint the location and nature of the pain and identify any associated symptoms. Laboratory tests play a crucial role. A complete Blood Count (CBC) typically reveals leukocytosis (an increased number of...
Diagnosing Appendicitis
It requires a multifaceted approach, starting with a detailed physical examination to pinpoint the location and nature of the pain and identify any associated symptoms. Laboratory tests play a crucial role. A complete Blood Count (CBC) typically reveals leukocytosis (an increased number of...
81
Cystic Fibrosis: Management
173
Cystic fibrosis (CF) is an autosomal recessive disorder that predominantly affects individuals of Northern European descent, occurring at a rate of 1 in 3500. It is caused by a genetic mutation in a gene on chromosome 7, most commonly the ΔF508 mutation, that codes for the cystic fibrosis transmembrane conductance regulator (CFTR) protein. This results in thicker mucus secretions and obstruction pathologies in multiple organs, including the lungs and sinuses.
Sinus disease and chronic...
Sinus disease and chronic...
173
Aneurysm III: Interprofessional Care
9
Aneurysm management involves either conservative medical therapy or surgical intervention, depending on the size and symptoms of the aneurysm. Conservative management is generally reserved for smaller, asymptomatic aneurysms, while larger or symptomatic aneurysms often necessitate surgical repair.Conservative Medical TherapyFor small, asymptomatic aneurysms, particularly abdominal aortic aneurysms (AAA) less than 5.5 centimeters in diameter, conservative medical therapy is recommended. This...
9

