双出口左心室:病例系列和对文献的系统审查
Michele Lioncino1, Giulio Calcagni1, Fausto Badolato1
1Pediatric Cardiology and Cardiac Arrhythmias and Syncope Unit, Bambino Gesù Children's Hospital, IRCSS, 00146 Rome, Italy.
Diagnostics (Basel, Switzerland)
|October 28, 2023
概括
这项研究详细介绍了双出口左心室 (DOLV),一种罕见的心脏缺陷. 肺狭窄和各种心室隔膜缺陷是常见的,影响儿科患者的手术结果.
科学领域:
- 儿童心脏病学 儿童心脏病学
- 遗传性心脏病是一种先天性心脏病.
- 心脏外科手术 心脏外科手术
背景情况:
- 双出口左心室 (DOLV) 是一种复杂的先天性心脏缺陷,其中两个大动脉都来自左心室.
- 了解DOLV的形态和相关异常对于诊断和手术规划至关重要.
研究的目的:
- 描述DOLV.的形态和成像特征.
- 评估相关形的患病率及其手术结果.
主要方法:
- 在Bambino Gesu儿童医院 (2011-2022) 的4个DOLV病例的回顾性审查.
- 对DOLV形态学和结果 (1975-2023) 的系统文献搜索 (MEDLINE,科学网络,EMBASE).
主要成果:
- 肺狭窄 (PS) 是最常见的相关病变 (75%的内部,69%的文献).
- 常见的VSD位置:下风口 (75%),肺下 (15%),双重承诺 (7%).
- 大动脉位置包括d-转移 (59%) 和l-转移 (35%).
结论:
- DOLV在形态和相关缺陷方面表现出显著的变化.
- 肺狭窄和下大动脉VSD在DOLV中非常普遍.
- 对于这种罕见的疾病,需要对手术结果进行进一步的研究.
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