单个系统的肺中朗格汉斯细胞囊细胞形成,只涉及气管支气管:一个病例报告
Xin Peng1,2, Hui Liu2, Xinyu Zhang3
1Department of Radiology, The Third People's Hospital of Chengdu, Chengdu, 610031, China.
BMC pulmonary medicine
|October 29, 2023
概括
肺部朗格汉斯细胞囊细胞症 (PLCH) 仅表现为气道加厚是罕见的. 早期诊断和治疗,包括切除和化疗,对于这种情况是有效的.
科学领域:
- 肺部病理学 肺部病理学
- 组织病理学 组织病理学
- 在瘤学瘤学.
背景情况:
- 肺部朗格汉斯细胞囊细胞形成 (PLCH) 通常涉及肺瘤.
- 孤立的气道干扰,表现为气管支气管壁加厚,是PLCH.的不常见表现.
研究的目的:
- 报告一种罕见的PLCH病例,其中完全涉及气道.
- 为了突出诊断和治疗策略的这个不寻常的演示.
主要方法:
- 一名26岁的非吸烟男性出现了喘息,咳和血.
- 诊断工作包括胸部CT,纤维光学支气管切除病变,组织病理学 (CD1a,S-100阳性) 和分子病理学 (BRAF V600E突变).
主要成果:
- 胸部CT显示了气管支气管壁的加厚和狭窄.
- 支气管镜检查显示了气管支气管树中的结节性瘤与正常的肺膜膜.
- 组织病理学和分子测试证实PLCH具有BRAF V600E突变.
结论:
- 应考虑在扩散的气管支气管病变的情况下进行PLCH,而没有肺瘤参与.
- 早期临床诊断和联合治疗 (切除和化疗) 对于有效的管理至关重要.
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