肺膜蛋白质结合性肺纤维化:进化变化和放射病学相关性
Eileen Hu-Wang1, Lydia Chelala1, Luis Landeras1
1From the Departments of Cardiopulmonary Imaging (E.H.W., L.C., L.L., J.H.C.), Pathology (H.L., A.N.H.), Pulmonary Medicine (M.E.S.), and Radiology (L.C.), The University of Chicago Medical Center, 5841 S Maryland Ave, Chicago, IL 60637.
Radiology. Cardiothoracic imaging
|November 1, 2023
概括
肺膜蛋白质病可以发展为肺纤维化,这是一个罕见的并发症. 这项研究详细介绍了使用CT成像的PAP-PF的三个病例,突出了其进展和病理.
科学领域:
- 罕见肺部疾病的放射学和病理学
背景情况:
- 肺膜蛋白质症 (PAP) 是一种罕见的疾病,往往具有良好的结果.
- 一小部分PAP患者患有肺纤维化 (PF),称为PAP-PF,使管理复杂化.
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