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Updated: Jul 11, 2025

Fluorescence-Based Measurements of Phosphatidylserine/Phosphatidylinositol 4-Phosphate Exchange Between Membranes
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通过将酸丁糖醇重塑与线粒体运输相结合,LPGAT1控制了MEGDEL综合征

Haoran Sun1, Jun Zhang2, Qianqian Ye3

  • 1Department of Biochemistry and Molecular Biology, Nanjing Medical University, Nanjing, 101 Longmian Avenue, Nanjing, Jiangsu Province 211166, China.

Cell reports
|November 2, 2023
PubMed
概括

LPGAT1催化了酸糖醇重塑,这对线粒体功能至关重要. 它的缺乏会导致MEGDEL综合征,因为它会破坏线粒体运输和状体结构.

关键词:
CP: 细胞生物学 细胞生物学在LPGAT1中使用LPGAT1.梅格德尔综合征是什么意思 梅格德尔综合征线粒体功能障碍 线粒体功能障碍酸糖醇是酸的原料之一.禁忌素/TIM复合物是一个复合物.

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