瓦萨尔瓦动脉瘤的突破性鼻与先天性心室隔膜缺陷并存:一个病例系列
Ni Made Ayu Wulan Sari1, Made Satria Yudha Dewangga2, Ida Bagus Rangga Wibhuti2
1Department of Cardiology and Vascular Medicine, Prof. Dr. I.G.N.G Ngoerah General Hospital, Diponogoro street, Denpasar, Bali, 80113, Indonesia. wulansari@unud.ac.id.
概括
瓦尔萨尔瓦动脉瘤 (RSoVA) 的鼻破裂经常发生在先天性心脏病 (CHD) 中,特别是心室隔膜缺陷 (VSD). 早期检测并存的CHD对于有效管理RSoVA患者出现呼吸短促至关重要.
科学领域:
- 心脏病学 心脏病学
- 心脏外科手术 心脏外科手术
- 医疗成像医学成像
背景情况:
- 瓦萨尔瓦动脉瘤突破性鼻 (RSoVA) 是一种罕见的心脏异常.
- RSoVA可以与先天性心脏病 (CHD) 并存,最常见的是心室隔膜缺陷 (VSD).
- 警的心声回声评估对于检测并存的心脏病和预防诊断监督至关重要.
研究的目的:
- 提出三例与VSD共存的RSOVA病例.
- 要突出诊断挑战和多式成像在识别共存的CHD多式成像的重要性.
- 强调在RSOVA患者中识别CHD的临床意义.
主要方法:
- 三名RSoVA和VSD患者的病例系列介绍.
- 使用诊断工具,包括右心脏和左心脏导管,心声学和跨食道心声学 (TEE).
- 采用多式成像技术,准确地界定了RSOVA和VSD之间的解剖关系.
主要成果:
- 这三名患者都出现了呼吸短促 (SOB).
- 诊断成像显示,在所有病例中,RSoVA与共存的VSD共存,其中一个VSD最初被缩的大动脉尖端掩盖.
- 一名患者有未经治疗的VSD病史,另一个患者在怀孕期间出现心力衰竭.
结论:
- RSoVA和VSD的组合经常具有症状,通常呈现为SOB.
- 准确诊断同时存在的CHD,如VSD,对于指导外科修复和管理策略至关重要.
- 综合诊断方法对于涉及RSoVA和相关心脏异常的综合患者护理至关重要.
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