脊髓灰质炎作为幼年系统性红斑狼的独特初始表现:病例报告
Hoda Tomoum1, Rasha El-Owaidy2, Abeer El-Zohiery3
1Pediatric Neurology Unit, Children's Hospital, Ain Shams University, Cairo, Egypt.
Lupus
|November 10, 2023
概括
青少年系统性红斑狼 (jSLE) 很少表现为多重神经病变. 这一案例突出了一个患有脑膜多神经炎的青少年作为jSLE的初始表现,成功地用免疫抑制剂治疗.
科学领域:
- 儿科风湿病学 儿科风湿病学
- 神经学 神经学
- 腎臟病學 (nephrology) 是一種醫學專業.
背景情况:
- 神经病是少年系统性红斑狼 (jSLE) 的不常见的初始表现.
- 在JSLE中,多重头骨神经的参与非常罕见.
研究的目的:
- 报告一个单一的脊髓炎 (PNC) 病例作为青少年jSLE的初始表现.
- 强调在儿科PNC的差异诊断中考虑jSLE的重要性.
主要方法:
- 一个青少年女性的病例报告呈现双边抽取和下神经病变的症状.
- 神经传导研究证实了部分轴突神经病变.
- 对jSLE的诊断是基于临床表现,阳性ANA,蛋白尿和组织检查结果 (III类狼性炎) 建立的.
主要成果:
- 患者表现出双边体和下神经病变,有电生理学证据表明左脸部和辅助神经受影响.
- 这种情况对脉冲甲基prednisolone和血交换有好反应.
- 通过脏活检诊断出III类狼性炎.
结论:
- 脑膜多神经炎可能是青少年jSLE的初始表现.
- 对于患有PNC的患者来说,早期识别和治疗jSLE至关重要.
- 这一案例强调了需要将原血管疾病纳入儿科神经病症的差异诊断中的必要性.
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