相关实验视频

Updated: Jul 11, 2025

Cystic Fibrosis Aggregate Biofilm Model to Study Infection-relevant Gene Expression
08:58

Cystic Fibrosis Aggregate Biofilm Model to Study Infection-relevant Gene Expression

Published on: April 18, 2025

522

[成年人的遗传扩散性囊性肺病]

R Diesler1, K Ahmad2, L Chalabreysse3

  • 1UMR754, INRAE, ERN-LUNG, service de pneumologie, centre de référence coordonnateur des maladies pulmonaires rares (OrphaLung), hôpital Louis-Pradel, Hospices civils de Lyon, université Lyon 1, Lyon, France.

Revue des maladies respiratoires
|November 11, 2023
PubMed
概括

多种囊性肺部疾病,包括淋巴结核病 (LAM) 和Birt-Hogg-Dubé综合征,具有共同的遗传联系和mTOR通路参与. 早期诊断和有针对性的治疗对于管理这些罕见的肺部疾病至关重要.

关键词:
伯特-霍格-杜贝是什么意思伯特 - 霍格 - 杜贝综合征扩散性囊性肺病是什么?遗传学 遗传学 是一种遗传学.遗传学是一种遗传学.间歇性肺病 间歇性肺病淋巴结核病是淋巴结核病的一种疾病.淋巴细胞流动性 淋巴细胞流动性 淋巴细胞流动性肺部囊性肺部疾病 (Maladie kystique pulmonaire) 是一种肺部疾病.肺炎病变 间隙性扩散性扩散性波恩维尔的结核菌管.结核性硬化综合体 结核性硬化综合体

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