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系统性初级卡尼丁缺乏症会导致严重的心律失常,原因是QT间隔缩短

Pierre Lodewyckx1, Jean Issa1, Margaux Gaschignard2

  • 1Institut des Cardiopathies Congénitales de Tours and FHU PRECICARE, CHU Tours, Tours, France.

Molecular genetics and metabolism
|November 18, 2023
PubMed
概括

系统性初级卡尼缺乏症 (PCD) 由于QT间隔缩短,导致危险的心律失常. 补充卡尼丁可以使QT间隔正常化,并防止患病患者发生致命的心脏事件.

关键词:
心肌病是一种心肌病.主要的肉素缺乏症.短QT综合征是什么突然死亡是突然死亡.腹腔动脉节律失常 腹腔动脉节律失常

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