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亚皮性缩性心肌病变:病理生理学,诊断和管理

Jiangtao Li^1,2,3, Jing Fang^1,2,3, Yani Liu⁴

¹Division of Cardiovascular Surgery, Tongji Hospital, Tongji Medical College, Huazhong University of Science and Technology, 1095 Jiefang Ave., Wuhan, 430030, China.

Clinical research in cardiology : official journal of the German Cardiac Society

|November 20, 2023

概括

亚皮性缩性心肌病 (Apical hypertrophic cardiomyopathy,ApHCM) 需要特定的诊断和管理指南. 这篇评论详细介绍了ApHCM的细节.

科学领域:

心脏病学心脏病学
遗传学遗传学是一个
医疗成像医学成像

背景情况:

亚皮性多变性心肌病 (Apical hypertrophic cardiomyopathy,ApHCM) 是一种多变性心肌病 (hypertrophic cardiomyopathy,HCM) 的独特亚型.
目前的指导方针提供有限的ApHCM特定的诊断和管理建议.
了解ApHCM的独特特征对于及时诊断和有效治疗至关重要.

研究的目的:

提供ApHCM的综合性审查,涵盖其发病率,病变发生和特征.
突出成像模式在ApHCM诊断中的作用.
介绍目前和新的管理策略,为ApHCM.

主要方法:

关于ApHCM发病率,病变发生和临床特征的文献综述.
分析成像技术,包括心声学和心血管磁共振成像 (CMR).
讨论ApHCM的既定和创新的治疗方法.

主要成果:

与其他HCM亚型相比,ApHCM具有独特的临床和病理特征.
心声学和CMR对于准确的ApHCM诊断至关重要.
一种新的穿性心跳隔膜肌切除手术显示出对ApHCM有希望的短期结果.

结论:

ApHCM需要量身定制的诊断和管理策略,超出一般的HCM指南.
先进的成像在表征ApHCM中起着至关重要的作用.
创新的外科手术技术,如跨管隔膜肌切除术,为ApHCM提供了新的治疗途径.

关键词:

状动脉瘤是指一个状动脉瘤.亚皮性过度缩性心肌病变.中腹腔阻塞和腔腔消灭.截面肌切除术截面肌切除术

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