在高输出心力衰竭的早产婴儿肝动脉静脉形形
Jessica Jakubowicz1, Ashley Lynch1, Kevin Wong1
1University of Arkansas for Medical Sciences/Arkansas Children's Hospital, Little Rock, AR, USA.
Global pediatric health
|December 11, 2023
概括
在早产婴儿中,先天性肝动脉静脉形 (HAVM) 是罕见的,并带有高死亡风险. 这一案例凸显了在一个非常早产的婴儿中管理这种情况的挑战,尽管及时干预.
科学领域:
- 血管外科 血管外科
- 新生儿心脏病学 新生儿心脏病学
- 儿科放射学 儿科放射学
背景情况:
- kongenital hepatic arteriovenous malformations (HAVM) 是一种罕见的血管异常,具有显著的死亡率,通常影响到到期的婴儿.
- 新生儿的症状性HAVM往往呈现为早期发作的充血性心力衰竭.
研究的目的:
- 报告一个非常早产婴儿的病例,在产前诊断出先天性肝动脉静脉形.
- 讨论HAVM在极低出生体重婴儿中的诊断和管理挑战.
- 突出产前诊断和多学科管理的关键重要性.
主要方法:
- 一个怀孕28周的婴儿因HAVM而患有高输出心力衰竭的案例报告.
- 产前诊断和手术前规划至关重要.
- 管理涉及药理学支持,透管栓塞,并试图部分栓塞.
主要成果:
- 婴儿出现了严重的高输出心力衰竭,这是HAVM的次要原因.
- 过导管封闭是在生命的第三天进行的.
- 尽管进行了最大限度的医疗管理和部分栓塞,但婴儿并没有存活.
结论:
- 先天性肝动脉静脉形形对非常早产的婴儿构成重大风险.
- 管理策略必须是个性化的,但结果仍然具有挑战性.
- 早期诊断和协调护理是必不可少的,尽管生存并不能保证.
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