一种罕见的系统性硬化症呈现
Joud Enabi1, Maha Tahir1, Srikanth Mukkera2
1Internal Medicine, Texas Tech University Health Sciences Center, Odessa, USA.
Cureus
|December 12, 2023
概括
系统性硬化症 (SSc) 可以影响心脏门,尽管大动脉门问题很少见. 这一案例凸显了需要门更换的SSc相关的大动脉反,强调早期检测以获得更好的患者结果.
科学领域:
- 心脏病学 心脏病学
- 类风湿病学 类风湿病学
- 自免疫性疾病 自免疫性疾病
背景情况:
- 系统性硬化症 (SSc) 是一种慢性自身免疫性疾病,其特征是纤维化影响各种器官.
- 心脏干扰在SSc中很常见,通常表现为膜疾病,特别是 mitra 门功能障碍.
研究的目的:
- 报告一个患有全身性硬化症的患者罕见的一例大动脉并发症.
- 强调识别不常见的SSc相关心脏表现的重要性.
- 突出对患者管理和治疗的临床影响.
主要方法:
- 一个47岁的男性患有渐进性系统性硬化症的病例报告.
- 对心脏并发症的临床评估.
- 通过左心房附属体活检确认心脏参与,显示纤维化.
主要成果:
- 该患者出现了系统性硬化症的次要心脏并发症.
- 左心房附属体活检证实了肌肉纤维化导致的心肌厚.
- 大动脉反需要大动脉门更换.
结论:
- 这一案例凸显了大动脉卷入系统性硬化症的可能性.
- 及时识别这种罕见的关联对于适当的患者管理至关重要.
- 识别和治疗SSc相关的大动脉反可以预防严重的并发症.
相关概念视频
01:20Myasthenia Gravis: Overview and Treatment
1.5K
Myasthenia gravis is a neuromuscular transmission disorder characterized by weakness and increased fatigability of skeletal muscles. It is an autoimmune disease affecting approximately one in 2000 people, where antibodies against the α1 subunit of nicotinic acetylcholine receptors are produced.
These antibodies interfere with the function of the nicotinic receptors in three ways: by binding to the receptor and disrupting acetylcholine binding; by causing cross-linking of receptors which...
These antibodies interfere with the function of the nicotinic receptors in three ways: by binding to the receptor and disrupting acetylcholine binding; by causing cross-linking of receptors which...
1.5K
01:18Disorders of the Autonomic Nervous System
655
The autonomic nervous system (ANS) is an intricate network of nerves that controls functions such as the regulation of heart rate, digestion, and blood pressure regulation. When this system malfunctions, it can lead to various disorders that affect multiple bodily functions. One common feature of many autonomic disorders is the involvement of smooth blood vessels, which play a crucial role in regulating blood flow throughout the body.
Raynaud's disease, also known as Raynaud's...
Raynaud's disease, also known as Raynaud's...
655