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Updated: Jul 8, 2025

Evaluation of Exon Inclusion Induced by Splice Switching Antisense Oligonucleotides in SMA Patient Fibroblasts
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努辛森在1型脊髓肌缩患者中诱导了复合运动动作潜能响应的可检测变化,这些患者的运动功能严重受损

Yuki Ueda1, Kiyoshi Egawa1, Kentaro Kawamura2

  • 1Department of Pediatrics, Hokkaido University Hospital, Sapporo, Japan.

Brain & development
|December 16, 2023
PubMed
概括

在1型严重脊髓肌缩 (SMA) 患者中,努辛森治疗通过微妙的肌肉运动改善了沟通. 纵向神经传导研究可以为这种复杂的患者群体提供客观的结果.

关键词:
复合动力动作潜力是一个复合动力动作潜力.神经传导研究的神经传导研究.这就是Nusinersen.运动功能的严重损伤.脊柱肌肉缩 脊柱肌肉缩 脊柱肌肉缩

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