肺部感染或炎症 - - 一个令人费解的MDA-5相关的青少年皮肤肌炎病例
Anusha Vuppala1, Manush Sondhi2, Sarwat Umer1
1Department of Rheumatology, Louisiana State University, Shreveport, LA, USA.
Pediatric rheumatology online journal
|December 21, 2023
概括
青少年皮肤肌炎 (JDM) 是一种罕见的自身免疫性疾病. 这一案例突出显示了通过传播性基因质等离子体症复杂化的JDM的管理,强调了结合抗真菌和免疫抑制疗法以改善结果.
科学领域:
- 儿科风湿病学 儿科风湿病学
- 传染性疾病 传染性疾病
- 肺部病理学 肺部病理学
背景情况:
- 青少年皮肤肌炎 (JDM) 是儿童罕见的自身免疫性肌肉病变,通过临床症状,肌肉酶升高和成像诊断.
- 在JDM中的自身抗体提供预后见解,但在儿童病例中不常见;MDA5抗体与间歇性肺病 (ILD) 有关.
- 标准的JDM治疗包括免疫抑制,常见的是葡萄糖皮质类药物和mycophenolate mofetil,以及IVIG用于耐火病例.
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