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Updated: Jul 7, 2025

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条纹偏向表达基因缺陷导致线粒体功能障碍在发育心肌细胞

Gu Li1,2, He Huang3,4, Yanshuang Wu1,4

  • 1Division of Newborn Medicine, Department of Pediatrics, Brigham and Women's Hospital, Boston, MA, 02115, USA.

Basic research in cardiology
|December 25, 2023
PubMed
概括

条纹偏向表达基因 (Speg) 缺陷会影响心肌细胞线粒体发育和能量代谢. 这导致线粒体结构异常,ATP生产减少,以及心脏发育中的心脏衰竭.

关键词:
扩展性心肌病变性是指扩展性心肌病变性线粒体中的线粒体.在PGC-1α酸化中.斯佩格 (Speg) 是一个名字.

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