在心房 Septal 缺陷装置关闭期间忽视了部分异常的肺静脉回归
Elahe Radmehr1,2, Hassan Radmehr3, Mohsen Shahidi4
1Colorectal Research Center, Imam Khomeini Hospital Complex, Tehran University of Medical Sciences, Tehran, Iran.
The journal of Tehran Heart Center
|December 26, 2023
概括
部分异常肺静脉回归 (PAPVR) 需要对心房隔膜缺陷 (ASD) 患者进行仔细评估. 一个案例强调了在ASD关闭期间需要解决PAPVR,以防止复杂的纠正程序.
科学领域:
- 心脏病学 心脏病学
- 遗传性心脏病是一种先天性心脏病.
背景情况:
- 部分异常肺静脉回归 (PAPVR) 是一种罕见的先天性心脏缺陷,肺静脉异常连接.
- PAPVR经常与心房隔膜缺陷 (ASD) 共存,需要在干预之前进行彻底评估.
- 如果在ASD与PAPVR同时未能诊断,可能会导致并发症,并需要复杂的纠正手术.
研究的目的:
- 描述一个10岁女孩患有PAPVR和secundum ASD的病例.
- 要突出在ASD设备关闭期间被忽视的PAPVR的挑战和管理.
- 强调ASD患者全面诊断的重要性.
主要方法:
- 一位患有PAPVR和ASD的儿科患者的病例报告.
- 审查PAPVR的诊断方式,包括心声和血管.
- 描述皮肤穿装置关闭ASD和随后的PAPVR的管理.
主要成果:
- 一名先前被忽视的PAPVR的10岁女孩接受了第二次ASD的设备关闭.
- 异常的静脉连接需要移除装置和复杂的纠正程序.
- 术后心声学证实肺静脉回归的成功纠正.
结论:
- 在所有被诊断为ASD的患者中,对PAPVR进行彻底的评估至关重要.
- 及时诊断和管理PAPVR可以防止需要复杂的干预措施.
- 先进的成像技术和仔细的程序内评估是识别PAPVR的关键.
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