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Updated: Jul 6, 2025

Modeling Charcot-Marie-Tooth Disease In Vitro by Transfecting Mouse Primary Motoneurons
07:43

Modeling Charcot-Marie-Tooth Disease In Vitro by Transfecting Mouse Primary Motoneurons

Published on: January 7, 2019

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神经纤维在健康和Charcot-Marie-Tooth病中的作用

Farah Kotaich1, Damien Caillol1, Pascale Bomont1

  • 1ERC team, NeuroMyoGene Institute-Pathophysiology and Genetics of Neuron and Muscle, Inserm U1315, CNRS UMR5261, University of Lyon 1, Lyon, France.

Frontiers in cell and developmental biology
|January 2, 2024
PubMed
概括

对于神经元结构和功能至关重要的神经纤维 (NFs) 被审查了它们的组装,运输和在神经退行性疾病 (如Charcot-Marie-Tooth (CMT)) 中的作用. 了解NF生物学为神经系统疾病提供治疗途径.

关键词:
在CMT上使用CMT.查洛特-玛丽-牙病是一种疾病.细胞骨架 细胞骨架动力学 动力学 动力学中间纤维丝是中间纤维丝.突变是发生在突变中的突变.神经退行性疾病的神经退行性疾病这是一个神经纤维神经纤维.

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