在没有智力障碍的古典银河血病患者中,社会认知,情绪调节和社会能力
Merel E Hermans1,2, Gert J Geurtsen3, Carla E M Hollak4
1Department of Paediatrics, Division of Metabolic Diseases, Amsterdam UMC Location University of Amsterdam, Emma Children's Hospital, Amsterdam, the Netherlands.
Acta neuropsychiatrica
|January 5, 2024
概括
经典银河血症 (CG) 患者报告社会满意度,但在社会认知方面表现出缺陷. 由于结果的多样性和自我与代理报告的差异,建议进行个性化神经心理评估.
科学领域:
- 代谢障碍 代谢障碍 代谢障碍
- 神经心理学 神经心理学
- 社会的认知社会认知.
背景情况:
- 经典的银河血症 (CG) 是一种代谢障碍,通常导致认知缺陷.
- 在CG患者中怀疑社会功能障碍,但证据有限.
- 了解CG中的社会能力对于长期的患者福祉至关重要.
研究的目的:
- 研究CG患者的社会认知,神经认知和情绪调节.
- 增强对古典银河血症患者社会能力的理解.
- 在CG中识别潜在的长期社会挑战.
主要方法:
- 对没有智力障碍的CG患者进行了全面的神经心理测试.
- 通过情绪识别,思维理论和同情度量 (自我和代理) 来评估社会认知.
- 将标准化患者结果与来自普通人群的规范性数据进行比较.
主要成果:
- 23名CG患者 (8-52岁) 参与了研究.
- CG患者报告了社会满意度,但社会认知 (情感识别,思想理论,同情心) 的缺陷.
- 成年人表现出较低的社会参与;父母报告儿童的社会功能和情绪调节较差.
结论:
- 尽管CG患者报告了社会满意度,但他们经常表现出社会认知缺陷.
- 自我报告和代理报告之间的显著变化和差异需要个性化评估.
- 为CG患者建议定制治疗计划,重点是全面的神经心理评估,包括社会认知.
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