免疫缺陷的胸腺瘤,联合扩散性泛支气管炎和成年人的潜伏性自身免疫糖尿病 - - 病例报告和系统审查
Yijiao Xu1, Lumin Wang1, Zhisheng Chen1
1Zhongshan Hospital (Xiamen), Fudan University, 361015, China.
Journal of translational autoimmunity
|January 8, 2024
概括
戈德综合征 (GS) 是一种罕见的胸腺瘤相关免疫缺陷. 这个案例突出了一个患有严重肺部感染和自身免疫糖尿病的患者,强调了GS免疫球蛋白治疗的诊断挑战和治疗潜力.
科学领域:
- 免疫学 免疫学 免疫学
- 内分泌学 在内分泌学.
- 肺部病理学 肺部病理学
背景情况:
- 戈德综合征 (GS) 是一种罕见的疾病,它将胸腺瘤和免疫缺陷联系在一起.
- 患者通常表现为胸腺瘤,减少B细胞,低血糖球蛋白血症和细胞介导免疫力受损.
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