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在意大利为患有PKU的婴儿提供无蛋白替代品是否相同?

Elvira Verduci1,2, Martina Tosi2,3, Chiara Montanari3,4

  • 1Metabolic Diseases Unit, Department of Pediatrics, Vittore Buzzi Children's Hospital, University of Milan, 20154 Milan, Italy.

Nutrients
|January 11, 2024
PubMed
概括

没有氨 (Phe) 的蛋白质替代品对于治疗婴儿PKU至关重要. 营养分析揭示了这些产品的显著差异,影响婴儿的健康和发育.

关键词:
没有的蛋白质替代品.阿拉基酸是一种生物学的生物学多可萨赫萨埃诺酸是什么意思婴儿营养 婴儿营养非传染性疾病的预防和预防.基尿症是什么? 基尿症是什么?

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