不是那么良性:一种罕见的异常异常外宫胆神经复合细胞瘤
R Patel1, D Lukins2, J L Villano3
1University of Louisville, Louisville, Kentucky, USA.
Journal of ophthalmology & visual sciences
|January 15, 2024
概括
一个罕见的非典型的状复合乳头瘤在大脑角呈现独特. 这一案例凸显了诊断方面的挑战以及瘤的攻击性,转移性潜力.
科学领域:
- 神经瘤学神经瘤学
- 神经外科 神经外科
- 病理学 病理学 病理学
背景情况:
- 冠状交错性乳头瘤 (CPPs) 是一种罕见的脑瘤,起源于冠状交错体上皮质.
- 非典型的CPP非常罕见,表现出高线粒活性和早期转移等侵略性特征.
- CPPs占所有脑瘤的0.4-0.6%,非典型变体占SEER数据库 (1978-2009) 中9%的病例.
研究的目的:
- 报告一种非典型的冠状动脉乳头瘤的独特病例.
- 为了突出其罕见的大脑角位置所带来的诊断挑战.
- 为了说明这种罕见瘤的临床过程和神经眼科表现.
主要方法:
- 一个56岁妇女的病例报告.
- 对临床表现,诊断成像和病理发现进行了审查.
- 关于非典型的冠状动脉乳头瘤和大脑角瘤的文献综述.
主要成果:
- 这位患者呈现出大脑角非典型的状结质乳头瘤,最初被误诊.
- 瘤呈现出勒普托门内斯种植,影响头骨神经和脊髓.
- 神经眼部并发症,包括乳头瘤和神经缺陷,逐渐发展.
结论:
- 非典型的冠状交叉体乳头瘤是罕见的,可以呈现出侵略性行为和转移.
- 宫外位置,如大脑角,带来了重大的诊断挑战.
- 这一案例强调了在具有挑战性的临床场景中考虑罕见诊断的重要性.
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