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Updated: Jul 5, 2025

Purification of Hsp104, a Protein Disaggregase
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Published on: September 30, 2011

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CLPB 分聚酶功能障碍影响蛋白质溶解性SPY复合物的功能完整性

Megan J Baker1, Kai Uwe Blau2,3, Alexander J Anderson1

  • 1Department of Biochemistry and Pharmacology and The Bio21 Molecular Science and Biotechnology Institute, The University of Melbourne, Parkville, Australia.

The Journal of cell biology
|January 25, 2024
PubMed
概括

线粒体分离酶CLPB的缺乏导致蛋白质聚合,并损害线粒体质量控制,这可能解释了相关的人类疾病,如3甲基谷酸尿症.

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