根据EULAR/ACR分类标准,在异常性炎症性肌肉病中出现EMG异常的频率
Keiichi Hokkoku1, Junpei Yamamoto1, Yudai Uchida1
1Department of Neurology, Teikyo University School of Medicine, Itabashi-ku, Tokyo, Japan.
Medicine
|January 26, 2024
概括
电肌图 (EMG) 经常显示出异常,特别是在患有异常性炎症性肌病 (IIM) 的患者中,特别是纤维化潜力和积极的尖波 (Fib/PSW). 这些发现对于诊断IIM至关重要,即使在不符合全部分类标准的情况下也是如此.
科学领域:
- 类风湿病学 类风湿病学
- 神经学 神经学
- 临床电生理学 临床电生理学
背景情况:
- 异常性炎症性肌肉病变 (IIM) 的诊断是使用欧洲反风湿联盟/美国风湿学会 (EULAR/ACR) 标准进行的.
- 电肌图 (EMG) 对于诊断IIM至关重要,但其与EULAR/ACR标准相关的发现需要进一步调查.
研究的目的:
- 在被诊断为IIM的患者中,确定特定EMG异常的频率,即纤维化潜力和正尖波 (Fib/PSW) 的频率.
- 在IIM的EULAR/ACR分类标准的背景下分析EMG发现.
主要方法:
- 对临床诊断为IIM的成年患者的临床和EMG记录的回顾性审查 (多质神经炎,皮质神经炎,氨基性皮质神经炎,包容性身体神经炎).
- 根据EULAR/ACR标准对患者进行分类.
- 在被招募的患者队列中调查Fib/PSW的频率.
主要成果:
- 在79名临床诊断为IIM的患者中,有75人符合确定的或可能的IIM标准.
- 在符合IIM标准的95%的患者中观察到动潜力和积极的尖波 (Fib/PSW).
- 在4名不符合足够的IIM概率标准的患者中也检测到Fib/PSW.
结论:
- 在根据IIM的EULAR/ACR标准分类的患者中,动潜力和正尖波 (Fib/PSW) 非常普遍.
- 电磁图谱的发现,特别是Fib/PSW,可以帮助检测IIM中的肌肉参与,包括在不完全满足分类标准的情况下.
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