第I类型获得的皮病:报告一个独特的渐进病例和简短的审查
Ana Lilia Peralta-Amaro1, Marissa de Jesús Quintal-Ramírez2, Alejandro Esteban-Prado1
1Internal Medicine Department, Hospital de Especialidades Centro Médico Nacional "La Raza", Instituto Mexicano del Seguro Social, Mexico City, Mexico; Division of Postgraduate Studies, Universidad Nacional Autónoma de México, Mexico City, Mexico.
The American journal of the medical sciences
|January 26, 2024
概括
获得性皮质松 (Acquired Cutis Laxa,ACL) 是一种罕见的结缔组织疾病,其病因尚不清楚. 本案例研究表明,免疫抑制疗法有效地管理了I型ACL患者的全身并发症.
科学领域:
- 皮肤病学 皮肤病学
- 结合组织疾病 结合组织疾病
- 罕见疾病 罕见疾病
背景情况:
- 松叶切割是一种罕见的结缔组织疾病,其特征是异常的弹性纤维,导致过早衰老.
- 它存在于遗传和获得的形式,而获得的切口关节 (ACL) 较为罕见,其病因不明.
- 系统性参与可以发生在ACL中,影响诸如脏,肺部和消化系统等器官.
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