一个带有状细胞的状形脂肉瘤病例:一个诊断陷
Takuma Arai1,2, Ikuma Kato2, Yusuke Kawabata3
1Department of Diagnostic Pathology, Yokohama City University Hospital, Yokohama, Japan.
International journal of surgical pathology
|February 5, 2024
概括
一种罕见的瘤Myxoid pleomorphic liposarcoma (MPLS) 可能会出现rhabdoid细胞,这可能会给诊断带来挑战. 识别这种组织学变异对于准确诊断和管理这种侵袭性癌症至关重要.
科学领域:
- 在瘤学瘤学.
- 病理学 病理学 病理学
- 遗传学 是一个遗传学.
背景情况:
- 状多样性脂肪瘤 (MPLS) 是一种极其罕见的瘤,在2020年世界卫生组织分类中被归类为.
- 在MPLS中,通常会呈现出状和形脂肪瘤样成分的混合物.
- 在遗传上,MPLS缺乏FUS/EWSR1::DDIT3融合和MDM2放大.
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