大人的大动脉扩张与修复的法洛特四重律:一个单中心研究
Tahereh Saedi1, Rashide Siami2, Amir J Ghaffari2
1Iran University of Medical Sciences, Tehran, Iran.
Cardiology in the young
|February 27, 2024
概括
大动脉扩张经常发生在已修复的四重法洛特病 (CHD) 的成年人中. 然而,在这些患者中,需要重新干预的严重的大动脉吐和剖析并不常见.
科学领域:
- 心脏病学 心脏病学
- 遗传性心脏病是一种先天性心脏病.
- 成年人的先天性心脏病
背景情况:
- 费洛特四重症是最常见的阴影性先天性心脏缺陷 (CHD).
- 手术修复允许大多数患者达到成年期.
- 经过修复的四重法洛特病的成年人通常需要重新干预残留异常,包括大动脉扩张.
研究的目的:
- 为了确定大动脉根扩张在已修复的法洛特四重律的成年人中的患病率.
- 在这个人群中评估大动脉扩张的结果,包括吐和剖析.
主要方法:
- 对730名患有Fallot四重律修复的患者进行了回顾性研究.
- 对大动脉尺寸的心声评估 (环,瓦萨尔瓦鼻,鼻管结,上升大动脉).
- 记录了大动脉吐和剖析的流行情况,需要重新干预.
主要成果:
- 瓦萨尔瓦扩张鼻的患病率为28.7%,上升大动脉21%,鼻管结8.3%,大动脉环1%.
- 在0.6%的患者中发生了严重的大动脉吐,需要进行手术修复.
- 一名患者出现了急性大动脉解剖.
结论:
- 大动脉扩张是成年人修复的Fallot四重律的常见发现.
- 由于大动脉扩张,吐或剖析,需要重新手术的需要很低.
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