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Updated: Jul 2, 2025

Rapid Generation of Amyloid from Native Proteins In vitro
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在不同的氨基烯菌中,依赖于肌纤维类型的"岩石"或"多层小石头"形成

Sharmistha Mitra1, Baozhi Chen2, John M Shelton3

  • 1Division of Neurology, Department of Pediatrics, University of Texas Southwestern Medical Center, 5323 Harry Hines Boulevard, Dallas, TX, 75390-9063, USA. sharmistha.mitra@utsouthwestern.edu.

Acta neuropathologica
|February 27, 2024
PubMed
概括

糖原结构是由酶维护的,而它们的缺失会导致氨基菌病,导致致命的神经系统疾病. 这项研究揭示了多糖的体型如何取决于小鼠的肌肉纤维类型和性别.

关键词:
纤维类型 纤维类型糖原代谢的代谢方式糖原储存疾病 糖原储存疾病多葡萄糖无糖是一种多糖无糖物质.骨架肌肉是一个骨肌肉.

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