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Updated: Jul 1, 2025

Phosphorus-31 Magnetic Resonance Spectroscopy: A Tool for Measuring In Vivo Mitochondrial Oxidative Phosphorylation Capacity in Human Skeletal Muscle
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Phosphorus-31 Magnetic Resonance Spectroscopy: A Tool for Measuring In Vivo Mitochondrial Oxidative Phosphorylation Capacity in Human Skeletal Muscle

Published on: January 19, 2017

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弗里德里希心脏衰竭中心脏发作的初始表现的表征

David R Lynch1,2,3, Sub Subramony4, Kimberly Y Lin5,6

  • 1Penn/CHOP Friedreich Ataxia Center of Excellence, Perelman School of Medicine, University of Pennsylvania, Philadelphia, PA, 19104, USA. lynchd@pennmedicine.upenn.edu.

Pediatric cardiology
|March 1, 2024
PubMed
概括

一些弗里德里希缺血症 (FRDA) 患者最初出现心脏问题,通常在诊断之前. 儿童心脏病学家的早期识别可以改善新FRDA疗法的结果.

关键词:
心肌病是一种心肌病.过度缩 过度缩 过度缩线粒体中的线粒体.在Omaveloxolone上使用.

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In Vivo Electrophysiological Measurement of Compound Muscle Action Potential from the Forelimbs in Mouse Models of Motor Neuron Degeneration06:35

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