婴儿持续性动脉静脉:重新考虑
Soliman Oushy1,2, Darren B Orbach3
1Department of Neurosurgery, Boston Children's Hospital, Harvard Medical School, Boston, Massachusetts, USA.
Journal of neurointerventional surgery
|March 7, 2024
概括
婴儿类型的持续动脉静脉突变 (IDAVS) 是罕见的儿科血管病变. 逐步栓塞提供了有利的结果,建议对更好的诊断和治疗进行修订分类.
科学领域:
- 儿科神经学 儿科神经学
- 血管外科 血管外科
- 神经辐射学神经辐射学
背景情况:
- 婴儿类型的持续动脉静脉突变 (IDAVS) 是一种罕见且异质的血管病变.
- 目前对儿科持续动脉静脉突变 (DAVS) 的分类系统由于呈现变化而不足.
- 这项研究旨在确定内血管治疗 (EVT) 后的IDAVS患病率和长期结果.
研究的目的:
- 为了估计婴儿类型持续动脉静脉突变 (IDAVS) 在儿科人口中的患病率.
- 评估IDAVS.的内血管治疗 (EVT) 后的长期临床和放射性结果.
- 建议对儿科持续动脉静脉突变 (DAVS) 进行修订的分类系统.
主要方法:
- 一个儿科脑血管数据库 (2006-2023) 的回顾性审查.
- 对IDAVS.表现和结果的临床和放射数据的分析.
- 评估内血管治疗 (EVT) 策略和结果.
主要成果:
- 在0.5%的患者 (8/1463) 中发现了IDAVS,平均年龄为34.7个月.
- 常见的表现包括大脑病 (37.5%) 和发作 (25%).
- 在87.5%的病例中进行了EVT,达到28.6%的放射性消灭和85.7%的良好临床结果 (mRS ≤2).
结论:
- IDAVS是一种罕见的,异质的儿科脑血管病理.
- 建议逐步选择性栓塞,而不是积极的方法,以获得有利的结果.
- 一个修订后的分类将儿科DAVS分为持续鼻发育不良和其他DAVS,提高了诊断清晰度和治疗方法.
相关概念视频
01:30Aneurysm I: Introduction
An aortic aneurysm is a localized outpouching or dilation at a weak point in the artery wall. It may involve different parts of the aorta, such as the abdominal aorta, aortic arch, or thoracic aorta.Etiological factorsSeveral disorders are associated with aortic aneurysms.Congenital causes, such as primary connective tissue disorders like Marfan syndrome, impact the integrity and strength of connective tissues, notably affecting the aorta. Marfan syndrome is a genetic disorder that specifically...
01:25Hemodialysis I: Introduction
Hemodialysis (HD) is a medical treatment that artificially removes waste products, excess fluids, and toxins from the blood when the kidneys are no longer able to perform these functions effectively. In this process, blood is filtered through a semipermeable membrane, allowing for the selective removal of waste while preserving necessary components like blood cells and proteins. Hemodialysis is typically performed in patients with end-stage renal disease (ESRD) or severe kidney...