结晶球蛋白血症血管炎与成人发病的斯蒂尔病相关
Noriharu Nakagawa1, Ai Fujii1,2, Yoshimichi Ueda3
1Department of Internal Medicine Keiju Medical Center Nanao Ishikawa Japan.
Clinical case reports
|March 8, 2024
概括
低血球性血管炎是成年人发病的斯蒂尔病 (AOSD) 的罕见并发症. 这一案例凸显了在AOSD患者呈现紫外线时考虑冷球蛋白血症血管炎的重要性.
科学领域:
- 类风湿病学 类风湿病学
- 血管炎是一种血管炎.
- 内部医学 内部医学
背景情况:
- 成人发病的斯蒂尔病 (AOSD) 是一种罕见的全身炎症疾病.
- 紫外线可能是AOSD血液学并发症的表现,包括血细胞综合征,扩散性血管内凝血或血栓性微血管病变.
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