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Updated: Jun 30, 2025

Using Scaffold Liposomes to Reconstitute Lipid-proximal Protein-protein Interactions In Vitro
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来自TID1S的可以在FRDA细胞模型中拯救frataxin缺乏和线粒体缺陷

Yi Na Dong1,2, Lucie Vanessa Ngaba1, Jacob An1

  • 1Department of Pediatrics and Neurology, The Children's Hospital of Philadelphia, Philadelphia, PA, United States.

Frontiers in pharmacology
|March 18, 2024
PubMed
概括

瘤形象性盘1 (TID1) 在弗里德里希的无氧症 (FRDA) 中负面控制了frataxin水平. TID1调制为这种遗传性神经退行性疾病提供了潜在的治疗策略.

关键词:
这就是ATPATPATP ATP.弗里德里希衰竭症 (FRDA) 是一种时间 时间弗拉塔克辛 (frataxin) 是一种线粒体碎片化的分裂

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