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Updated: Jun 29, 2025

Author Spotlight: Studying the Impact of Maternal Dietary Deficiencies on Long-Term Offspring Health Outcomes
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Published on: June 28, 2024

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在Phenylketonuria患者中的同型氨酸和甲基马龙酸

Giovana Regina Weber Hoss1,2, Fernanda Sperb-Ludwig1,2, Tássia Tonon1

  • 1Hospital de Clínicas de Porto Alegre, Laboratório BRAIN, Porto Alegre, RS, Brazil.

Genetics and molecular biology
|April 9, 2024
PubMed
概括

用代谢配方治疗的基尿症 (PKU) 患者很少表现出增加的总同型氨酸 (tHcy) 或维生素B12缺乏. 坚持饮食是控制这些水平和预防并发症的关键.

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