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氧化/阿米奥达龙对法布里小鼠的酶替代疗法的疗效有影响吗?

Takahiro Tsukimura1, Koki Saito1, Tomoko Shiga2

  • 1Department of Functional Bioanalysis, Meiji Pharmaceutical University, 2-522-1 Noshio, Kiyose, Tokyo 204-8588, Japan.

Molecular genetics and metabolism reports
|April 11, 2024
PubMed
概括

使用复合人类α-galactosidase A (α-Gal) 治疗法布里病的酶替代疗法 (ERT) 可能与基 (HCQ) 或阿米奥达龙 (AMI) 联合使用. 在体内研究表明,在Fabry小鼠中对ERT疗法的有效性没有任何不良影响.

关键词:
艾米奥达龙是一种阿米奥达龙.阴阳性两性药物 阴阳性两性药物药物诱导的脂化症酶替代疗法是一种酶替代疗法.费布里病是什么意思 费布里病是什么意思甘氨基脂是葡萄糖基脂中的一种.氧化chloroquine 的使用情况.α-Galactosidase A 是一种酶.

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