:

Adrien Joseph1,2, Stéphanie Harel3, Laurent Mesnard2,4,5

  • 1Service de Médecine intensive réanimation, Hôpital Saint Louis, Assistance Publique des Hôpitaux de Paris, Paris, France.

概括

卡菲尔佐米布相关的血栓性微血管病变 (CFZ-TMA) 通常会导致严重的急性损伤. 补充路径变异和eculizumab治疗似乎没有影响这种罕见疾病的预后.

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