刚硬的右心房综合征? 一个复杂的临床病例报告,利用多模式成像和侵入性血液动力学
Krithika Krishnarao1,2, Daniel S Yip2, Rohan M Goswami2
1Department of Cardiovascular Disease, Orlando Health Heart & Vascular Institute, 1222 S Orange Ave 1st floor, Orlando, FL 32806, USA.
刚性右心房综合征,一种导致心力衰竭的新型疾病,在心脏移植患者身上描述. 这种综合症的特征是右心房硬化,通过心脏和脏移植成功治疗.
科学领域:
- 心脏病学 心脏病学
- 移植医学 移植医学
- 心脏生理学 心脏生理学
背景情况:
- 硬左心房综合征是心力衰竭的已知原因之一.
- 之前没有记录过影响右心房的类似情况.
- 这一案例涉及耐火性右心衰竭,发生在心脏移植术后12年.
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