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Updated: Jun 26, 2025

Analysis of Mitochondrial Respiratory Chain Complexes in Cultured Human Cells using Blue Native Polyacrylamide Gel Electrophoresis and Immunoblotting
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在复杂I组合和线粒体疾病中对NDUFAF6的系统分析

Andrew Y Sung1, Rachel M Guerra2, Laura H Steenberge3

  • 1Department of Biomolecular Chemistry, University of Wisconsin School of Medicine and Public Health, Madison, WI, USA.

Nature metabolism
|May 8, 2024
PubMed
概括

复杂I组合因子 (CIAF) 的缺陷导致线粒体疾病. 这项研究揭示了NDUFAF6在复杂I组合中的作用,确定NDUFS8是关键相互作用,并为诊断NDUFAF6相关疾病提供了资源.

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