异位突变型肺骨化作为间歇性肺异常的表型:CT-病理相关性和患病率
Midori Ueno1, Ryoko Egashira2, Mikiko Hashisako3
1Department of Radiology, University of Occupational and Environmental Health School of Medicine, 1-1 Iseigaoka, Kitakyushu City, Fukuoka, 807-8555, Japan. mueno@med.uoeh-u.ac.jp.
在CT扫描上,异形树突状肺骨化 (DPO) 与骨化和纤维化相对应. 这种情况在9.2%的间歇性肺异常 (ILA) 病例中发现,这表明DPO是ILA的表型.
科学领域:
- 肺部医学 肺部医学
- 放射学 放射学是一门学科.
- 病理学 病理学 病理学
背景情况:
- 异形突变性肺骨化 (DPO) 往往无症状,并且在肺部CT扫描中偶尔发现.
- 缺乏精确的CT-病理相关性和患病率数据,用于特异性DPO.
研究的目的:
- 为了澄清异常性DPO的组织学背景.
- 为了确定异常性DPO的患病率.
主要方法:
- 将HRCT的发现与16名已确诊的异常性DPO患者的组织学数据进行比较.
- 评估了8111名接受CT扫描进行转移查的患者间歇性肺异常 (ILA) 和DPO的患病率.
主要成果:
- 在组织学上,DPO与骨化和痕组织性肺炎/纤维化有关.
- 在大多数情况下,CT上发现了分支,圆形或线性结构.
- 在9.2%的ILA患者 (所有病例的0.3%) 中存在DPO.
结论:
- 在CT上,异形性DPO显示骨化和纤维化.
- 在9.2%的ILA案件中,DPO被确定.
- 异常性DPO被认为是ILAs的病理表型.
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