相关实验视频

Updated: Jun 26, 2025

Author Spotlight: Three-Dimensional Cephalometric Landmark Annotation Demonstration on Human Cone Beam Computed Tomography Scans

Author Spotlight: Three-Dimensional Cephalometric Landmark Annotation Demonstration on Human Cone Beam Computed Tomography Scans

Published on: September 8, 2023

法克斯综合征和多区域性牙发育不良:一个病例报告

Jean Marie Star¹, Richard C Jordan², Ray E Stewart¹

¹Department of Orofacial Sciences, University of California San Francisco, San Francisco, CA 94143, USA.

The Journal of clinical pediatric dentistry

|May 17, 2024

概括

本病例报告详细介绍了一种罕见的PHACES综合征 (后腔形,血管瘤,动脉异常,大动脉/心脏缺陷的协,眼睛异常,骨形) 在幼儿中与多区域性牙发育不良同时发生.

科学领域:

医学遗传学医学遗传学
儿科牙科儿科牙科
发展生物学发展生物学

背景情况:

法克斯综合征是一种罕见的多系统性疾病,其特征是特定的先天异常.
婴儿血瘤和区域性牙扩张 (鬼牙) 是不同的发育状况.
PHACES综合征和牙发育不良的同时发生是非常罕见的.

研究的目的:

报告一个罕见的PHACES综合征病例与同时存在的多区域牙发育不良.
以突出牙科管理挑战在这样复杂的案例.
强调在综合症患者中需要跨学科的护理.

主要方法:

一个被诊断患有PHACES综合征的两岁男孩的案例介绍.
牙异常的临床和放射评估.
在全身麻醉下手术切除严重受影响的母牙.

主要成果:

这位患者出现了PHACES综合征和十颗失塑牙 (50%的牙).
受影响的母牙表现出敏感性,形成,长期预后不佳.
对所有受影响的母牙进行了拔除.

结论:

这一案例强调了PHACES综合征与广泛的牙发育不良之间罕见的关联.
早期诊断和干预对于治疗综合征患者的牙科并发症至关重要.
对于患有复杂先天性疾病的儿童的长期牙科护理和发育,多学科的方法至关重要.

关键词:

牙异常是一种牙异常.牙发育不良症是指牙发育不良症.这就是法克斯综合征.

更多相关视频

Systematic Assessment of Mammalian Skull Specimens for Dental and Temporomandibular Joint Pathology

Systematic Assessment of Mammalian Skull Specimens for Dental and Temporomandibular Joint Pathology

Published on: August 22, 2022

Treatment of Facial Deformities using 3D Planning and Printing of Patient-Specific Implants

Treatment of Facial Deformities using 3D Planning and Printing of Patient-Specific Implants

Published on: May 23, 2020

相关概念视频

Teeth

Teeth

The formation of teeth, also known as odontogenesis, is a complex process that begins in utero, around the sixth week of embryonic development. There are three stages to this process: the bud stage, the cap stage, and the bell stage.
In the bud stage, the tooth germ (an aggregation of cells) starts to form in the developing jawbone. During the cap stage, the tooth germ differentiates into enamel organ, dental papilla, and dental sac, which will later develop into the tooth's enamel, dentin...