单态表皮性肠道T细胞淋巴瘤 (MEITL) 复杂,肠道阻塞和穿孔
Macarena Soto Dopazo1, Yaiza Rey Fanjul2, Pablo Chamorro Chamorro3
1Cirugía General y del Aparato Digestivo, Hospital Universitario de Cabueñes, España.
Revista espanola de enfermedades digestivas
|May 20, 2024
概括
本病例报告详细介绍了一名被诊断患有单形上皮质型肠道T细胞淋巴瘤 (MEITL) 的患者,这是一种罕见且具有攻击性的瘤. 治疗包括手术切除,化疗和干细胞移植.
科学领域:
- 胃肠病学 胃肠病学
- 在瘤学瘤学.
- 病理学 病理学 病理学
背景情况:
- 单形表皮性肠道T细胞淋巴瘤 (MEITL) 是一种罕见的肠道瘤.
- 它的特征是内皮细胞淋巴细胞的增殖,预后不好.
- 腹部症状通常是不特定的,使早期诊断复杂化.
研究的目的:
- 报告MEITL二次性肠道阻塞病例与封闭的穿孔.
- 突出与这种罕见淋巴瘤相关的诊断和治疗挑战.
- 讨论目前对MEITL的介绍和管理的理解.
主要方法:
- 诊断了一名患有腹部疼痛,口腔不耐受和血的便的患者.
- 诊断工作包括成像和活检.
- 进行了手术腹腔切除术以进行瘤切除和分期.
主要成果:
- 这名患者被诊断出患有导致阻塞的状瘤,并含有穿孔.
- 活检证实了单形上皮质型肠道T细胞淋巴瘤 (MEITL).
- 瘤涉及阴,小肠中也有类似的病变.
结论:
- MEITL是一种罕见的T细胞淋巴瘤,具有非特异性症状和严重的并发症,如穿孔和阻塞.
- 多模式治疗,包括手术,化疗和干细胞移植,往往是必要的.
- 需要进一步的研究来建立MEITL的标准治疗方法.
相关概念视频
Esophageal Perforation-II: Clinical Manifestations and Management
56
Esophageal perforations manifest in various clinical forms, influenced by factors such as the perforation's cause and location (cervical, intrathoracic, or intra-abdominal), the extent of contamination, and potential injury to adjacent mediastinal structures. The timing between the perforation occurrence and treatment initiation also affects the clinical presentation.
Clinical Manifestations:
Clinical Manifestations:
56
Esophageal Perforation-I: Introduction
87
Esophageal perforation is a severe medical condition characterized by a breach in the integrity of the esophageal wall. This breach can occur due to various factors such as trauma, medical procedures, or underlying diseases. When the esophageal wall is compromised, it allows food, fluids, and digestive juices into the chest cavity or adjacent structures, leading to potential complications and health risks.
The location of esophageal perforation can vary, occurring anywhere along the esophagus....
The location of esophageal perforation can vary, occurring anywhere along the esophagus....
87
Inflammatory Bowel Disease I: Ulcerative Colitis
165
Introduction
Inflammatory bowel disease, or IBD, encompasses a group of disorders characterized by chronic inflammation or ulceration of the gastrointestinal tract.
Risk Factors
The exact cause of IBD remains unclear, although it is believed to be due to a mix of genetic, environmental, microbial, and immune factors. Genetic factors are significant in determining susceptibility to IBD, with family history being a critical risk factor. Individuals with a first-degree relative who has IBD are at...
Inflammatory bowel disease, or IBD, encompasses a group of disorders characterized by chronic inflammation or ulceration of the gastrointestinal tract.
Risk Factors
The exact cause of IBD remains unclear, although it is believed to be due to a mix of genetic, environmental, microbial, and immune factors. Genetic factors are significant in determining susceptibility to IBD, with family history being a critical risk factor. Individuals with a first-degree relative who has IBD are at...
165
Inflammatory Bowel Disease V: Surgical Management
144
Surgical interventions for inflammatory bowel disease (IBD), which includes ulcerative colitis and Crohn's disease, are essential in managing symptoms and addressing complications. The selection of surgical procedures is contingent upon the specific conditions and complications that stem from these illnesses.
Here are some common surgical interventions for IBD:
Here are some common surgical interventions for IBD:
144
Chronic Bowel Disorders: Introduction
442
Chronic bowel diseases are a group of long-term conditions affecting the digestive tract, characterized by inflammation and damage to the gut lining. These conditions primarily include irritable bowel syndrome and inflammatory bowel disease.
Irritable Bowel Syndrome (IBS) is a common disorder affecting the gastrointestinal tract. The distinctive feature is recurrent abdominal pain associated with altered bowel movements, manifesting as constipation, diarrhea, or fluctuating between both. The...
Irritable Bowel Syndrome (IBS) is a common disorder affecting the gastrointestinal tract. The distinctive feature is recurrent abdominal pain associated with altered bowel movements, manifesting as constipation, diarrhea, or fluctuating between both. The...
442
Inflammatory Bowel Disease II: Crohn's Disease
217
Introduction
Inflammatory bowel disease, commonly known as IBD, refers to a collection of disorders that lead to persistent inflammation of the gastrointestinal tract. The two types of IBD are ulcerative colitis, which impacts the colon, and Crohn's disease, which can involve any part of the gastrointestinal segment.
Crohn's disease
Crohn's disease is a chronic, systemic inflammatory bowel disease (IBD) that predominantly affects the gastrointestinal tract. It is marked by...
Inflammatory bowel disease, commonly known as IBD, refers to a collection of disorders that lead to persistent inflammation of the gastrointestinal tract. The two types of IBD are ulcerative colitis, which impacts the colon, and Crohn's disease, which can involve any part of the gastrointestinal segment.
Crohn's disease
Crohn's disease is a chronic, systemic inflammatory bowel disease (IBD) that predominantly affects the gastrointestinal tract. It is marked by...
217


