拉巴洛斯科普的 inguinal 带 thanatophoric 发育不良:一个案例报告
Keiichiro Tanaka1, Kumpei Abe1, Masato Koizumi2
1Department of Pediatric Surgery, Seirei Hamamatsu General Hospital, Shizuoka, Japan.
Asian journal of endoscopic surgery
|June 5, 2024
概括
超性发育不良 (TD) 是一种严重的骨疾病. 这份报告详细介绍了TD患者1岁男孩的第一个腹腔镜带术,展示了一种新的外科手术方法.
科学领域:
- 医学遗传学 医学遗传学
- 儿科手术 儿科手术
- 骨发育不良症 骨发育不良症
背景情况:
- 太那托福性失育症 (TD) 是一种罕见的,致命的骨失育症,其特征是严重的微粒细胞,巨头和胸部缺血.
- 新生儿由于肺部低成形导致的呼吸衰竭是TD中死亡的主要原因.
- 在TD幸存者的手术干预通常仅限于维持生命的手术,如气管切除术或心室分离术.
关键词:
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