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Updated: May 13, 2026

An In Vitro Model for the Study of Cellular Pathophysiology in Globoid Cell Leukodystrophy
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在人类亨廷顿病皮质中的微质增殖和星球细胞蛋白质变化

Adelie Y S Tan1, Lynette J Tippett2, Clinton P Turner3

  • 1Centre for Brain Research, University of Auckland, Auckland 1023, New Zealand; Department of Anatomy and Medical Imaging, University of Auckland, Auckland 1023, New Zealand.

Neurobiology of disease
|June 6, 2024
PubMed
概括

亨廷顿病 (HD) 涉及皮质微质,可能是由微质增殖驱动的. 星球细胞显示质纤维酸性蛋白 (GFAP) 表达变化,与突变的亨廷丁 (mHTT) 水平有关.

关键词:
格里奥斯症是发生在细胞上的一种.人类大脑组织人脑组织亨廷顿病就是亨廷顿病.中间状回环 中间状回环核武器的扩散组织微阵列组织微阵列.

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