皮肤放射学评估先天性四肢过度生长的血管综合征
Suryansh Arora1, Shibani Mehra1, Ipshita Bhattacharya2
1Department of Radiodiagnosis, ABVIMS and Dr. RML Hospital, New Delhi, Delhi, India.
Indian dermatology online journal
|June 7, 2024
概括
先天性四肢过度生长血管综合征 (CLOS) 是一种罕见的疾病,导致四肢过度生长. 这项研究详细介绍了五例CLOS病例,强调需要进行全面的临床和放射性评估,以获得更好的患者结果.
科学领域:
- 血管生物学和医学 血管生物学和医学
- 遗传学和罕见疾病
- 儿科综合征学 儿科综合征学
背景情况:
- 先天性四肢过度生长的血管综合征 (CLOS) 是一种罕见的,复杂的疾病,其特点是四肢单边扩大和其他异常.
- CLOS包括几个不同的综合征,包括Klippel-Trenaunay综合征,Parkes-Weber综合征,CLOVES综合征,Proteus综合征,PTEN Hamartomatous综合征和纤维脂肪系血管异常.
- 由于这些综合征的复杂性,有效的管理需要采用多学科的方法.
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