胆道 - 形形综合征 (BASM):一个病例报告
Hadeil Alhashmi1, Esra Chawshly1, Süleyman Çelebi1
1Faculty of Medicine, Altinbas University, Bahcelievler Mahallesi, E-5 Karayolu, Kultur Sokak, No: 1, 34180 Bahcelievler, Istanbul, Turkey.
International journal of surgery case reports
|June 23, 2024
概括
胆管缩和形形 (BASM) 综合征需要早期诊断和治疗以获得更好的结果. 迅速的手术干预,如Kasai portoenterostomy,对于管理新生儿这种情况至关重要.
科学领域:
- 新生儿胆固醇症的发生.
- 儿科外科手术 儿科外科手术
- 胃肠病学 胃肠病学
背景情况:
- 胆管缩 (BA) 呈现为持续的新生儿胆固醇黄,增加肝病和门性高血压风险.
- 胆管缩和形缺陷综合征 (BASM) 是一种严重的BA形式,预后较差,如果不治疗,可能导致肝硬化和肝衰竭.
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