一个关于Senear-Usher综合征的病例报告
Shivani D Jangid1, Bhushan Madke1, Adarshlata Singh1
1Dermatology, Venereology, and Leprosy, Jawaharlal Nehru Medical College, Datta Meghe Institute of Higher Education and Research, Wardha, IND.
Cureus
|July 3, 2024
概括
红斑,一种罕见的自身免疫性皮肤疾病,呈现出与狼的独特重叠. 这份病例报告详细介绍了一名被诊断患有这种疾病的患者,强调了关键的诊断标志物和成功的免疫抑制治疗.
科学领域:
- 皮肤病学 皮肤病学
- 自体免疫学 自体免疫学
- 皮肤疾病的病理生理学
背景情况:
- 红斑虫 (PE) 是一种罕见的自身免疫性突发性疾病.
- 乳腺发育与红性狼和状虫共享临床,组织学和血清学特征.
- PE中的自身抗原包括desmoglein 3,desmoglein 1和desmosomal粘附蛋白,破坏了角质细胞的粘附并引起了acantholysis.
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