脏的desmoplastic小圆细胞瘤:一个病例报告和讨论
Guizhen Huang1, Wenqian Huang1, Mingxue Liu1
1Department of Pediatric Surgery, The First Affiliated Hospital of Xiamen University, Xiamen University, Xiamen, Fujian, China.
Frontiers in oncology
|July 5, 2024
概括
一种罕见的脏癌症 - - 脱质小圆细胞瘤 (DSRCT) 在一个13岁的男孩身上被诊断出. 治疗包括手术,化疗 (CAV-VIP),放射治疗和针对骨转移的向治疗 (anlotinib).
科学领域:
- 儿科瘤学 儿科瘤学
- 医疗成像医学成像
- 手术瘤学手术瘤学
背景情况:
- 一名13岁的男孩出现了部和部疼痛,以及低烧.
- 最初的成像显示左脏恶性瘤与广泛的转移.
研究的目的:
- 报告一个起源于脏的脱质小圆细胞瘤 (DSRCT) 病例.
- 描述这种罕见的儿科癌症的多模式治疗方法.
主要方法:
- 诊断证实了正子发射断层扫描-计算机断层扫描 (PET-CT) 和术后病理学.
- 治疗包括左切除术,交替CAV-VIP化疗,脱手术,放射治疗和向治疗.
主要成果:
- 病理诊断证实了原发性脏脱质小圆细胞瘤 (DSRCT).
- 多式疗法实现了腹部瘤的初始控制,但骨转移仍然存在.
- 该患者目前正在治疗骨转移的anlotinib.
结论:
- 型小圆细胞瘤 (DSRCT) 是一种攻击性的恶性瘤,很少在脏中出现.
- 包括手术,化疗,放射治疗和向治疗在内的综合模式方法对于管理高级DSRCT至关重要.
- 需要进行持续的研究,以改善DSRCT骨转移的治疗策略.
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